|
Behcet Syndrome
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Disease • C0004943
Definition
A rare chronic inflammatory disorder of unknown etiology. It is characterized by the development of ulcers in the mouth and genital region and uveitis. Other signs and symptoms include arthritis, deep vein thrombosis and superficial thrombophlebitis.
Synonyms
Behcet Syndrome • Behcet's Syndrome • Behcets Syndrome • Triple-Symptom Complex • triple symptom complex • Behcet Disease • Behcet's disease • Behçet's disease • ADAMANTIADES-BEHCET SYNDROME • BEHCET TRIPLE SYMPTOM COMPLEX • BEHCET RECURRENT DISEASE • OCULOBUCCOGENITAL SYNDROME • Behcet's • BD • BEHCET DIS • Behcet Syndrome [Disease/Finding]
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|
HLA-B gene
IL10 gene
Mouth Diseases
Colchicine
Vasculitis
Skin Diseases, Vascular
Sulfasalazine
Anterior uveitis
Azathioprine
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Related concepts
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#
|
Concept name
|
Type
|
Relation
|
Support
|
Score
|
|
1
|
Azathioprine
|
Compound
|
Known
|
Explain
|
34.62630
|
|
2
|
Anterior uveitis
|
Disease
|
Known
|
Explain
|
28.47762
|
|
3
|
Sulfasalazine
|
Compound
|
Known
|
Explain
|
23.35403
|
|
4
|
Colchicine
|
Compound
|
Known
|
Explain
|
15.98927
|
|
5
|
Skin Diseases, Vascular
|
Disease
|
Known
|
Explain
|
14.71432
|
|
6
|
Vasculitis
|
Disease
|
Known
|
Explain
|
10.06678
|
|
7
|
Mouth Diseases
|
Disease
|
Known
|
Explain
|
6.73663
|
|
8
|
Thionucleosides
|
Compound
|
Inferred
|
Explain
|
3.12512
|
|
9
|
mercaptopurine
|
Compound
|
Inferred
|
Explain
|
2.72852
|
|
10
|
IL10 gene
|
Gene
|
Known
|
Explain
|
1.86942
|
|
11
|
HLA-B gene
|
Gene
|
Known
|
Explain
|
1.56012
|
|
12
|
Iridocyclitis
|
Disease
|
Inferred
|
Explain
|
1.31085
|
|
13
|
Iritis
|
Disease
|
Inferred
|
Explain
|
1.31085
|
|
14
|
Iris Diseases
|
Disease
|
Inferred
|
Explain
|
1.10558
|
|
15
|
Pancreatitis
|
Disease
|
Inferred
|
Explain
|
0.97728
|
|
16
|
Panuveitis
|
Disease
|
Inferred
|
Explain
|
0.76684
|
|
17
|
Arteritis
|
Disease
|
Inferred
|
Explain
|
0.31269
|
|
18
|
Malignant Atrophic Papulosis
|
Disease
|
Inferred
|
Explain
|
0.24678
|
|
19
|
Mucocutaneous Lymph Node Syndrome
|
Disease
|
Inferred
|
Explain
|
0.21597
|
|
20
|
Giant Cell Arteritis
|
Disease
|
Inferred
|
Explain
|
0.19926
|
|
21
|
Polyarteritis Nodosa
|
Disease
|
Inferred
|
Explain
|
0.18747
|
|
22
|
Takayasu Arteritis
|
Disease
|
Inferred
|
Explain
|
0.16845
|
|
23
|
Livedo Reticularis
|
Disease
|
Inferred
|
Explain
|
0.16713
|
|
24
|
Sneddon Syndrome
|
Disease
|
Inferred
|
Explain
|
0.16418
|
|
25
|
Inflammatory Bowel Diseases
|
Disease
|
Inferred
|
Explain
|
0.13762
|
|
26
|
Vasculitis, Central Nervous System
|
Disease
|
Inferred
|
Explain
|
0.13261
|
|
27
|
Sulfonamides
|
Compound
|
Inferred
|
Explain
|
0.13079
|
|
28
|
Systemic Vasculitis
|
Disease
|
Inferred
|
Explain
|
0.12210
|
|
29
|
SLC46A1 gene
|
Gene
|
Inferred
|
Explain
|
0.11342
|
|
30
|
Pyoderma Gangrenosum
|
Disease
|
Inferred
|
Explain
|
0.10617
|
|
31
|
Ulcerative Colitis
|
Disease
|
Inferred
|
Explain
|
0.09355
|
|
32
|
VASCULITIS, LYMPHOCYTIC, CUTANEOUS SMALL VESSEL
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Disease
|
Inferred
|
Explain
|
0.08625
|
|
33
|
VASCULITIS, LYMPHOCYTIC, NODULAR
|
Disease
|
Inferred
|
Explain
|
0.08625
|
|
34
|
Thioinosine
|
Compound
|
Inferred
|
Explain
|
0.08577
|
|
35
|
Angiomatosis, Bacillary
|
Disease
|
Inferred
|
Explain
|
0.08558
|
|
36
|
Thiouridine
|
Compound
|
Inferred
|
Explain
|
0.08013
|
|
37
|
Facial Nerve Diseases
|
Disease
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Inferred
|
Explain
|
0.06591
|
|
38
|
Rheumatoid Arthritis
|
Disease
|
Inferred
|
Explain
|
0.06173
|
|
39
|
TRAF1 gene
|
Gene
|
Inferred
|
Explain
|
0.05433
|
|
40
|
MYT1 gene
|
Gene
|
Inferred
|
Explain
|
0.05282
|
|
41
|
Phlebitis
|
Disease
|
Inferred
|
Explain
|
0.05263
|
|
42
|
Hypersensitivity vasculitis
|
Disease
|
Inferred
|
Explain
|
0.05170
|
|
43
|
Vasculitis Adverse Event
|
Disease
|
Inferred
|
Explain
|
0.05068
|
|
44
|
Aortitis
|
Disease
|
Inferred
|
Explain
|
0.05000
|
|
45
|
Thromboangiitis Obliterans
|
Disease
|
Inferred
|
Explain
|
0.04884
|
|
46
|
Arterial Occlusive Diseases
|
Disease
|
Inferred
|
Explain
|
0.04796
|
|
47
|
Shwartzman Phenomenon
|
Disease
|
Inferred
|
Explain
|
0.04700
|
|
48
|
Nucleosides
|
Compound
|
Inferred
|
Explain
|
0.04693
|
|
49
|
Oral Hemorrhage
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Disease
|
Inferred
|
Explain
|
0.04672
|
|
50
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Retinal Vasculitis
|
Disease
|
Inferred
|
Explain
|
0.04611
|
|
51
|
Learning Disorders
|
Disease
|
Inferred
|
Explain
|
0.04589
|
|
52
|
Henoch-Schoenlein Purpura
|
Disease
|
Inferred
|
Explain
|
0.04586
|
|
53
|
NAT2 gene
|
Gene
|
Inferred
|
Explain
|
0.04535
|
|
54
|
Lymphocyte
|
Other
|
Inferred
|
Explain
|
0.04516
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|
55
|
Oral Manifestations
|
Disease
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Inferred
|
Explain
|
0.04270
|
|
56
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NFATC4 gene
|
Gene
|
Inferred
|
Explain
|
0.04245
|
|
57
|
Facial Hemiatrophy
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Disease
|
Inferred
|
Explain
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0.03795
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|
58
|
Melkersson-Rosenthal Syndrome
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Disease
|
Inferred
|
Explain
|
0.03795
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|
59
|
Oral Fistula
|
Other
|
Inferred
|
Explain
|
0.03629
|
|
60
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Aortic Arch Syndromes
|
Disease
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Inferred
|
Explain
|
0.03612
|
|
61
|
Bell Palsy
|
Disease
|
Inferred
|
Explain
|
0.03452
|
|
62
|
Facial Neuralgia
|
Disease
|
Inferred
|
Explain
|
0.03275
|
|
63
|
Ophthalmia, Sympathetic
|
Disease
|
Inferred
|
Explain
|
0.03101
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|
64
|
Lichen Planus, Oral
|
Disease
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Inferred
|
Explain
|
0.03098
|
|
65
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Lip Diseases
|
Disease
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Inferred
|
Explain
|
0.03093
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|
66
|
Salivary Gland Diseases
|
Disease
|
Inferred
|
Explain
|
0.03017
|
|
67
|
AIDS Arteritis, Central Nervous System
|
Disease
|
Inferred
|
Explain
|
0.02992
|
|
68
|
RELA gene
|
Gene
|
Inferred
|
Explain
|
0.02880
|
|
69
|
Oral Ulcer
|
Disease
|
Inferred
|
Explain
|
0.02858
|
|
70
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Urticaria
|
Disease
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Inferred
|
Explain
|
0.02857
|
|
71
|
Tuberculosis, Oral
|
Disease
|
Inferred
|
Explain
|
0.02854
|
|
72
|
Hemifacial Spasm
|
Disease
|
Inferred
|
Explain
|
0.02782
|
|
73
|
Uveitis, Posterior
|
Disease
|
Inferred
|
Explain
|
0.02768
|
|
74
|
Aortic Diseases
|
Disease
|
Inferred
|
Explain
|
0.02760
|
|
75
|
Ludwig's Angina
|
Disease
|
Inferred
|
Explain
|
0.02737
|
|
76
|
Oculovestibuloauditory syndrome
|
Disease
|
Inferred
|
Explain
|
0.02712
|
|
77
|
Stomatitis
|
Disease
|
Inferred
|
Explain
|
0.02689
|
|
78
|
Ranula (disorder)
|
Disease
|
Inferred
|
Explain
|
0.02649
|
|
79
|
Facial paralysis
|
Disease
|
Inferred
|
Explain
|
0.02647
|
|
80
|
Oral candidiasis
|
Disease
|
Inferred
|
Explain
|
0.02626
|
|
81
|
Iris Neoplasms
|
Disease
|
Inferred
|
Explain
|
0.02583
|
|
82
|
RALBP1 gene
|
Gene
|
Inferred
|
Explain
|
0.02530
|
|
83
|
Liver Cirrhosis, Experimental
|
Disease
|
Inferred
|
Explain
|
0.02523
|
|
84
|
CD59 gene
|
Gene
|
Inferred
|
Explain
|
0.02506
|
|
85
|
Peripheral Vascular Diseases
|
Disease
|
Inferred
|
Explain
|
0.02482
|
|
86
|
Mouth, Edentulous
|
Disease
|
Inferred
|
Explain
|
0.02454
|
|
87
|
Immune Complex Diseases
|
Disease
|
Inferred
|
Explain
|
0.02431
|
|
88
|
Vascular Diseases
|
Disease
|
Inferred
|
Explain
|
0.02415
|
|
89
|
Warfarin
|
Compound
|
Inferred
|
Explain
|
0.02412
|
|
90
|
Mucositis
|
Disease
|
Inferred
|
Explain
|
0.02280
|
|
91
|
Iridocorneal endothelial syndrome
|
Other
|
Inferred
|
Explain
|
0.02196
|
|
92
|
Periodontal Diseases
|
Disease
|
Inferred
|
Explain
|
0.02090
|
|
93
|
Uveal Diseases
|
Disease
|
Inferred
|
Explain
|
0.02072
|
|
94
|
Heparin
|
Compound
|
Inferred
|
Explain
|
0.02027
|
|
95
|
Uveitis
|
Disease
|
Inferred
|
Explain
|
0.02013
|
|
96
|
Alkaloids
|
Compound
|
Inferred
|
Explain
|
0.01975
|
|
97
|
TAT gene
|
Gene
|
Inferred
|
Explain
|
0.01937
|
|
98
|
Exfoliation Syndrome
|
Disease
|
Inferred
|
Explain
|
0.01927
|
|
99
|
Inosine
|
Compound
|
Inferred
|
Explain
|
0.01896
|
|
100
|
IL1B gene
|
Gene
|
Inferred
|
Explain
|
0.01755
|
|